Granulomatosis with polyangiitis, a new nomenclature for Wegener's Granulomatosis - Case report
AUTOR(ES)
Lima, Alexandre Moretti de, Torraca, Pedro de Freitas Silva, Rocha, Sheila Pereira da, Santiago, Carmelia Matos Reis, Ferraz, Fabio Humberto Ribeiro Paes
FONTE
An. Bras. Dermatol.
DATA DE PUBLICAÇÃO
2015-06
RESUMO
AbstractThe granulomatosis with polyangiitis, initially known as Wegener's granulomatosis, is a small and medium vessels vasculitis. It's classic form presents a triad: necrotizing granuloma of respiratory tract, necrotizing cutaneous vasculitis and glomerulonephritis. This vasculitis has cytoplasmic antineutrophil antibodies as signal. This work illustrates a case, of multisystemic rare disease, in which the segment and treatment were considered satisfactory for symptoms remission.