Progressive hemifacial atrophy with agenesis of the head of the caudate nucleus.
AUTOR(ES)
Leäo, M
RESUMO
We describe a woman with right hemifacial atrophy, a high palate, partial left motor seizures, and mild atrophy of the left arm. CT scan showed asymmetrical lateral ventricles and MRI (magnetic resonance imaging) showed atrophy of the right cerebral hemisphere and agenesis of the head of the right caudate nucleus. To our knowledge, this is the first report of Parry-Romberg syndrome associated with structural abnormalities of the basal nuclei documented by MRI. We suggest that a neurovascular aetiology can explain the spectrum of segmental defects associated with hemifacial atrophy.
ACESSO AO ARTIGO
http://www.pubmedcentral.nih.gov/articlerender.fcgi?artid=1016702Documentos Relacionados
- Hemichorea reversible after operation in a boy with cavernous angioma in the head of the caudate nucleus.
- A compulsive movement disorder with cavitation of caudate nucleus.
- Progressive hemifacial atrophy: a case report.
- Some observations on the aetiology of progressive hemifacial atrophy ("Parry-Romberg syndrome")
- Distinct presynaptic control of dopamine release in striosomal and matrix areas of the cat caudate nucleus.