Lymphangioleiomyomatosis
Mostrando 1-12 de 21 artigos, teses e dissertações.
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1. Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
ABSTRACT CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior
Sao Paulo Med. J.. Publicado em: 15/01/2018
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2. Incidental detection of retroperitoneal lymphangioleiomyomatosis (LAM) - CT and MRI findings with relevance to the urologist
Int. braz j urol.. Publicado em: 2014-08
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3. Avaliação de hiperinsuflação dinâmica em pacientes com linfangioleiomiomatose através de teste de exercício cardiopulmonar e verificação da resposta à broncodilatação / Evaluation of dynamic hyperinflation in patients with lymphangioleiomyomatosis with cardiopulmonary exercise testing and verification of the response to bronchodilator
INTRODUÇÃO: Linfangioleiomiomatose (LAM) é uma doença rara, caracterizada pela proliferação de células musculares lisas atípicas ao redor de vias aéreas, vasos sanguíneos e linfáticos, com formação de cistos pulmonares difusos. Na prova de função pulmonar (PFP), a doença se caracteriza por padrão obstrutivo, aprisionamento aéreo e redução
IBICT - Instituto Brasileiro de Informação em Ciência e Tecnologia. Publicado em: 23/10/2012
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4. Avaliação dos efeitos da doxiciclina sobre o bloqueio de metaloproteinases e na evolução funcional das pacientes com linfangioleiomiomatose / Evaluation of treatment with doxycycline over metalloproteinase blockage and functional assessment in patients with lymphangioleiomyomatosis
A Linfangioleiomiomatose (LAM) é uma rara afecção, caracterizada pela substituição do parênquima pulmonar por cistos, resultando em prejuízo na troca gasosa e progressiva piora funcional. A patogênese da formação dos cistos permanece incerta, mas tem sido associada à hiperreatividade de metaloproteinases (MMP), principalmente MMP-2 e -9. Neste est
IBICT - Instituto Brasileiro de Informação em Ciência e Tecnologia. Publicado em: 31/08/2011
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5. Pulmonary arterial involvement leading to alveolar hemorrhage in lymphangioleiomyomatosis
Clinics. Publicado em: 2011
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6. Avaliação da função pulmonar, sono, exercício e qualidade de vida em pacientes com linfangioleiomiomatose pulmonar / Lung function, sleep, six-minute walk test and quality of life (SF-36) evaluation in pulmonary lymphangioleiomyomatosis
A linfangioleiomiomatose pulmonar é uma enfermidade cística progressiva que afeta mulheres jovens e cuja sobrevida média estimada em algumas casuísticas é de cerca de dez anos após o diagnóstico. A deterioração da função pulmonar é uma de suas principais características e resulta em dispnéia progressiva e hipoxemia grave nos casos avançados. O
Publicado em: 2008
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7. Haemopericardium and cardiac tamponade complicating pulmonary lymphangioleiomyomatosis.
A case of pulmonary lymphangioleiomyomatosis complicated by haemopericardium and cardiac tamponade is reported. This was successfully managed by creating a subdiaphragmatic extraperitoneal window.
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8. Comparison of the use of antibodies to alpha smooth muscle actin and desmin in pulmonary lymphangioleiomyomatosis.
To establish if antibodies to alpha smooth muscle actin (ASMA) are better than desmin as a tumour marker in pulmonary lymphangioleiomyomatosis both antisera were applied to five cases. ASMA strongly stained the muscle in all cases but desmin was negative. Five cases of cryptogenic fibrosing alveolitis showed that mature smooth muscle embedded in fibrous tiss
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9. Metastatic endometrial stromal sarcoma masquerading as pulmonary lymphangioleiomyomatosis.
A 39 year old female presented with bilateral pneumothoraces and interstitial shadowing on chest x ray. A diagnosis of lymphangioleiomyomatosis was made following an open lung biopsy. Over the next eight years she developed respiratory failure leading to single lung transplantation but she died in the immediate postoperative period. Necropsy examination and
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10. Lymphangioleiomyomatosis presenting in a postmenopausal woman.
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11. Pneumothorax After Air Travel in Lymphangioleiomyomatosis, Idiopathic Pulmonary Fibrosis, and Sarcoidosis
American College of Chest Physicians.
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12. Relation of pulmonary lymphangio-leiomyomatosis to use of the oral contraceptive pill and fertility in the UK: a national case control study.
BACKGROUND--Pulmonary lymphangioleiomyomatosis is a rare progressive disease of unknown aetiology affecting premenopausal women. Since the oral contraceptive pill has been implicated in its pathogenesis, a case control study was carried out to determine whether women with the disease were more likely to have taken the oral contraceptive pill, and whether the