Rosai Dorfman
Mostrando 1-12 de 20 artigos, teses e dissertações.
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1. Generalized erythematous and scaly plaques and papules: a rare case of Rosai-Dorfman disease accompanied by multiple myeloma
Abstract: A 75-year-old male presented with generalized erythematous, scaly plaques and painless lymphadenopathy. Rosai-Dorfman disease was suspected based on clinical manifestations and confirmed by histopathologic and immune reactivity studies performed on the biopsy obtained from the left supraclavicular lymph node. The patient was also diagnosed with mul
An. Bras. Dermatol.. Publicado em: 2018-06
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2. Histological variability and the importance of clinicopathological correlation in cutaneous Rosai-Dorfman disease
Abstract: Rosai-Dorfman disease is a benign histiocytic proliferative disorder of unknown etiology. The disease mainly affects lymph node tissue, although it is rarely confined to the skin. Here, we describe a 53-year-old woman with purely cutaneous Rosai-Dorfman disease. The patient presented with a large pigmented plaque on her left leg, and sparse erythem
An. Bras. Dermatol.. Publicado em: 2016-10
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3. Doença de Rosai-Dorfman acometendo fossas nasais e seios paranasais
Radiol Bras. Publicado em: 2016-08
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4. Rosai-Dorfman disease: a report of eight cases in a tertiary care center and a review of the literature
Rosai-Dorfman disease (RDD) is a nonmalignant histiocytic disorder of unknown origin that is extremely rare. By immunohistochemistry, the RDD cells are characteristically S-100 positive and CD1a negative. Emperipolesis is a common histopathological finding, although not specific for RDD. Lymph node and cutaneous manifestations are most frequent, but diverse
Braz J Med Biol Res. Publicado em: 10/10/2014
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5. Histiocitoses: uma revisão focada em achados de neuroimagem
Objetivo: Histiocitose é uma doença sistêmica que, frequentemente, acomete o sistema nervoso central. Este trabalho propõe discutir as características de neuroimagem da histiocitose de células de Langerhans (HCL), mais comum; e as histiocitoses não-Langerhans (HNL), como a síndrome hemofagocítica, doenças de Erdheim-Chester e Rosai-Dorfman. Mé
Arq. Neuro-Psiquiatr.. Publicado em: 2014-07
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6. Case for diagnosis
Cutaneous Rosai-Dorfman disease is a rare, lymphoproliferative disease. It is benign and self-limited, only involves skin and subcutaneous tissue and typically occurs as histiocyte-rich inflammatory infiltrates, manifesting as erythematous to brown papules, plaques, or nodules, without predilection for site. The authors describe a case of cutaneous Rosai-Dor
An. Bras. Dermatol.. Publicado em: 2014-01
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7. Sinus Histiocytosis with Massive Lymphadenopathy (Rosai-Dorfman Disease): A Case Report and Literature Review
Introduction Rosai-Dorfman disease (RDD) is a rare histiocytic proliferative disorder of unknown etiology. Usually it presents with massive painless cervical lymph node enlargement. Histologically, it shows proliferation of distinctive histiocytic cells that demonstrate emperipolesis in the background of a mixed inflammatory infiltrates. Immunohistochemical
Int. Arch. Otorhinolaryngol.. Publicado em: 2014
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8. Doença de Rosai-Dorfman com manifestação cutânea extensa - Relato de caso
A doença de Rosai-Dorfman é uma desordem benigna, autolimitada, idiopática, decorrente da proliferação de histiócitos. Foi descrita pela primeira vez por Rosai e Dorfman em 1969. Tipicamente, a doença se caracteriza por extensa linfadenopatia cervical, febre, gamopatia monoclonal e leucocitose com neutrofilia. Manifestações extranodais são encontra
An. Bras. Dermatol.. Publicado em: 2013-04
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9. Rosai-Dorfman em seios paranasais como diagnóstico diferencial de polipose nasosinusal na infância
Brazilian Journal of Otorhinolaryngology. Publicado em: 2012-06
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10. Doença de Rosai-Dorfman cutânea: relato de caso e revisão de literatura
Relata-se o caso de uma paciente com doença de Rosai-Dorfman cutânea que apresentava na região glútea direita uma placa eritemato-acastanhada infiltrada com áreas amareladas e pápulas eritemato-acastanhadas perilesionais. O exame anatomopatológico revelou infiltrado inflamatório predominantemente de linfócitos e histiócitos de citoplasma amplo, cla
Jornal Brasileiro de Patologia e Medicina Laboratorial. Publicado em: 2011-02
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11. Acometimento orbitário na doença de Rosai-Dorfman
A doença de Rosai-Dorfman (DRD) ou histiocitose sinusal com linfadenopatia maciça é uma entidade clínica idiopática, rara e benigna, caracterizada pela proliferação histiocitária com linfofagocitose. Geralmente se apresenta com linfoadenomegalia cervical, no entanto pode haver acometimento extranodal, sendo a região orbitária um dos locais de poss�
Revista Brasileira de Oftalmologia. Publicado em: 2011-02
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12. Rosai-Dorfman disease with spontaneous resolution: case report of a child
Rosai-Dorfman disease is a self-limiting condition caused by histiocyte proliferation within the sinusoids of lymph nodes and in extranodal tissue. It is a rare disease, particularly in children, that progresses with extensive lymphadenopathy. This paper reports on the case of a 2-year-old child with progressive cervical lymphadenopathy associated with persi
Revista Brasileira de Hematologia e Hemoterapia. Publicado em: 2011